FOREWARNED IS FOREARMED: MRI PRACTICAL ASPECTS IN HIRAYAMA DISEASE
Abstract
Hirayama disease (HD) is a rare neurological condition typically thought to be endemic for South Asia andJapanregion. Disease is characterized by juvenile muscular atrophy of unilateral distal upper extremity with benign course. MRI of the cervical spine is the way to confirm HD in clinically supposed case. Some typical MR-signs can be visualized in neutral position (abnormal cervical curvature, loss of attachment between the posterior dural sac and subjacent lamina, localized lower cervical cord atrophy with asymmetric spinal cord flattening and hyperintensity) and in flexion position (anterior shifting of the posterior dura and posterior epidural space enlargement). Here we describe 5 HD cases in Russian population with a detailed MRI description and MRI protocol recommendations in case of HD suspicion.
About the Authors
E. I. Kremneva
Research Center of Neurology
Russian Federation
Russian Federation
A. A. Vorobyeva
Research Center of Neurology
Russian Federation
Russian Federation
L. S. Adarycheva
Research Center of Neurology
Russian Federation
Russian Federation
R. N. Konovalov
Research Center of Neurology
Russian Federation
Russian Federation
A. S. Suslin
Research Center of Neurology
Russian Federation
Russian Federation
M. V. Krotenkova
Research Center of Neurology
Russian Federation
Russian Federation
M. N. Zakharova
Research Center of Neurology
Russian Federation
Russian Federation
D. A. Grishina
Research Center of Neurology
Russian Federation
Russian Federation
A. L. Antelava
Research Center of Neurology
Russian Federation
Russian Federation
V. V. Bryukhov
Research Center of Neurology
Russian Federation
Russian Federation
A. V. Terehov
The first Republican clinical hospital of Ministry of health of the Udmurt Republic
Russian Federation
Russian Federation
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Review
For citations:
Kremneva E.I., Vorobyeva A.A., Adarycheva L.S., Konovalov R.N., Suslin A.S., Krotenkova M.V., Zakharova M.N., Grishina D.A., Antelava A.L., Bryukhov V.V., Terehov A.V. FOREWARNED IS FOREARMED: MRI PRACTICAL ASPECTS IN HIRAYAMA DISEASE. Diagnostic radiology and radiotherapy. 2015;(3):35-43. (In Russ.)
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