Difficulties in the differential diagnosis of multiple sclerosis and Susak syndrome
https://doi.org/10.22328/2079-5343-2020-12-1-24-29
Abstract
Retino-cochleo-cerebral angiopathy or Susac syndrome is a rare autoimmune disease that selectively affects the vessels of the retina, the inner ear and the central nervous system. Differentiation of Susac syndrome and multiple sclerosis presents difficulties due to the similarity of MRI semiotics of these two diseases. This article presents two clinical cases of patients with Susac syndrome who were diagnosed with multiple sclerosis at the onset of the disease. Based on the analysis of our own clinical observations and literature data, the issues of differential diagnosis of Susac syndrome and multiple sclerosis are highlighted. For the first time a variant of the MRI picture transformation in Susac syndrome is presented.
About the Authors
Zh. I. Savintseva
N.P. Bechtereva Institute of the Human Brain of the Russian Academy of Sciences
Russian Federation
Russian Federation
Zhanna I. Savintseva.
St. Petersburg.
A. G. Ilves
N.P. Bechtereva Institute of the Human Brain of the Russian Academy of Sciences
Russian Federation
Russian Federation
Alexander G. Ilves.
St. Petersburg.
V. M. Lebedev
N.P. Bechtereva Institute of the Human Brain of the Russian Academy of Sciences
Russian Federation
Russian Federation
Valery M. Lebedev.
St. Petersburg.
O. M. Novoselova
N.P. Bechtereva Institute of the Human Brain of the Russian Academy of Sciences
Russian Federation
Russian Federation
Olga M. Novoselova.
St. Petersburg.
L. N. Prakhova
N.P. Bechtereva Institute of the Human Brain of the Russian Academy of Sciences
Russian Federation
Russian Federation
Liidia N. Prakhova.
St. Petersburg.
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Review
For citations:
Savintseva Zh.I., Ilves A.G., Lebedev V.M., Novoselova O.M., Prakhova L.N. Difficulties in the differential diagnosis of multiple sclerosis and Susak syndrome. Diagnostic radiology and radiotherapy. 2021;12(1):24-29. (In Russ.) https://doi.org/10.22328/2079-5343-2020-12-1-24-29
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