Involvement of the central nervous system in patient with chronic inflammatory demyelinating polyneuropathy: a case report
https://doi.org/10.22328/2079-5343-2022-13-3-77-87
Abstract
Chronic inflammatory demyelinating polyneuropathy (CIDP) is an uncommon disease characterized by heterogeneous clinical findings, absence of specific laboratory markers and good response to treatment. Typically CIDP manifests as weakness of varying severity, from minimal paresis to plegia, as well as symmetrical loss of sensitivity in all limbs, a distinctive clinical feature of CDL is the involvement of both proximal and distal parts of extremities. At the same time, there is a large number of atypical CIDP variants, clinically similar to other chronic disimmune neuropathies. Neuroimaging findings typically include involvement of the cauda equina, brachial, and lumbar plexus. The patient sought medical help complaining of weakness and loss of sensation in the extremities. This clinical case illustrates a combined involvement of cranial and spinal nerves, as well as spinal cord and brain in a patient with chronic inflammatory demyelinating polyneuropathy.
Keywords
About the Authors
T. M. RostovtsevaRussian Federation
Tatiana M. Rostovtseva — radiologist, research assistant of the department of radiologic and radionuclide diagnostic methods of the FCBN of the FMBA of Russian Federation; SPIN code 5840–7590.
117513, Moscow, Ostrovityanova str. 1, b.10
M. B. Dolgushin
Russian Federation
Mikhail B. Dolgushin — Dr. of Sci. (Med.), professor of the Russian Academy of Sciences, head of the department of radiologic and radionuclide diagnostic methods of the FCBN of the FMBA of Russian Federation; SPIN code 6388–9644.
117513, Moscow, Ostrovityanova str. 1, b. 10
A. V. Lopatina
Russian Federation
Anna V. Lopatina — neurologist of the FCBN of the FMBA of RF.
117513, Moscow, Ostrovityanova str. 1, b. 10
O. V. Boyko
Russian Federation
Olga V. Boyko — Dr. of. Sci. (Med.), head of the neurological department of the FCBN of the FMBA RF.
117513, Moscow, Ostrovityanova str. 1, b.10
E. A. Kovrazhkina
Russian Federation
Elena A. Kovrazhkina — Cand. of Sci. (Med.), senior research assistant of the scientific and research laboratory of clinical neurophysiology of the FCBN of the FMBA RF.
117513, Moscow, Ostrovityanova str. 1, b.10
S. A. Gulyaev
Russian Federation
Sergey A. Gulyaev — Dr. of Sci. (Med.), head of the scientific and research laboratory of clinical neurophysiology of the FCBN of the FMBA RF; SPIN code 6645–2922.
117513, Moscow, Ostrovityanova str. 1, b. 10
A. N. Boyko
Russian Federation
Alexey N. Boyko — Dr. of Sci. (Med.), professor, director of the institute of clinical neuroimmunology, head of the department of neuroimmunology of the FCBN of the FMBA RF; SPIN code 9921–9109.
117513, Moscow, Ostrovityanova str. 1, b. 10
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Review
For citations:
Rostovtseva T.M., Dolgushin M.B., Lopatina A.V., Boyko O.V., Kovrazhkina E.A., Gulyaev S.A., Boyko A.N. Involvement of the central nervous system in patient with chronic inflammatory demyelinating polyneuropathy: a case report. Diagnostic radiology and radiotherapy. 2022;13(3):77-87. (In Russ.) https://doi.org/10.22328/2079-5343-2022-13-3-77-87