Multimodality imaging in apical hypertrophic cardiomyopathy: clinical case
F. N. Chanakhchian, 
N. I. Gulyaev,
D. V. Slivinski,
I. V. Klochkova,
E. V. Shutova,
A. Yu. Demchenkova
N. I. Gulyaev,
D. V. Slivinski,
I. V. Klochkova,
E. V. Shutova,
A. Yu. Demchenkova https://doi.org/10.22328/2079-5343-2023-14-3-93-98
Abstract
Apical hypertrophic cardiomyopathy is rare familial form of hypertrophic cardiomyopathy, with hypertrophy mainly affecting the apex of the left ventricle and characterized by a spade-like left ventricular cavity. Despite varying presentation, impaired capabilities of some standard instrumental methods and dissent on diagnostic criteria several diagnostic characteristics estimated by various noninvasive imaging modalities make it possible to establish a diagnosis with high accuracy. We hereby describe a case with electrocardiographic abnormalities and chest pain with suspected acute coronary syndrome. Acute coronary syndrome was excluded as well as performing invasive coronary angiography was avoided using advanced diagnostic tools including single photon emission computed tomography and apical hypertrophic cardiomyopathy was demonstrated by careful differential diagnosis.
About the Authors
F. N. Chanakhchian
National medical research center of high medical technologies — The Vishnevsky central military clinical hospital
Russian Federation
Russian Federation
Flora N. Chanakhchian — Cand. of Sci. (Med.), Head of emission computed tomography laboratory at the Department of radioisotope diagnostics
Kranogorsk
N. I. Gulyaev
National medical research center of high medical technologies — The Vishnevsky central military clinical hospital
Russian Federation
Russian Federation
Nikolay I. Gulyaev —Dr. of Sci. (Med.), сardiology center officer, Senior cardiologist FGFI «NMRC HMT n.a. A. A. Vishnevsky» ; professor at the Emergency department in Military Medical Academy named after S. M. Kirov
Kranogorsk
D. V. Slivinski
National medical research center of high medical technologies — The Vishnevsky central military clinical hospital
Russian Federation
Russian Federation
Dmitriy V. Slivinski — Cand. of Sci. (Med.),Head of cardiology department
Kranogorsk
I. V. Klochkova
National medical research center of high medical technologies — The Vishnevsky central military clinical hospital
Russian Federation
Russian Federation
Inna V. Klochkova — Cand. of Sci. (Med.), Cardiologist
Kranogorsk
E. V. Shutova
National medical research center of high medical technologies — The Vishnevsky central military clinical hospital
Russian Federation
Russian Federation
Elena V. Shutova — Head of UD (heart) in Functional Diagnostic Center
Kranogorsk
A. Yu. Demchenkova
National medical research center of high medical technologies — The Vishnevsky central military clinical hospital
Russian Federation
Russian Federation
Anna Yu. Demchenkova — Cand. of Sci. (Med.), Radiologist
Kranogorsk
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Review
For citations:
Chanakhchian F.N., Gulyaev N.I., Slivinski D.V., Klochkova I.V., Shutova E.V., Demchenkova A.Yu. Multimodality imaging in apical hypertrophic cardiomyopathy: clinical case. Diagnostic radiology and radiotherapy. 2023;14(3):93-98. (In Russ.) https://doi.org/10.22328/2079-5343-2023-14-3-93-98
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